3HAD101_m

3-hydroxyacyl-[acyl-carrier-protein] dehydratase (C10:1(2E) forming)(mitochondrial)

3HAD121_m

3-hydroxyacyl-[acyl-carrier-protein] dehydratase (C12:1(2E) forming)(mitochondrial)

3HAD141_m

3-hydroxyacyl-[acyl-carrier-protein] dehydratase (C14:1(2E) forming)(mitochondrial)

3HAD161_m

3-hydroxyacyl-[acyl-carrier-protein] dehydratase (C16:1(2E) forming)(mitochondrial)

3HAD41_m

3-hydroxyacyl-[acyl-carrier-protein] dehydratase (C4:1(2E) forming)(mitochondrial)

3HAD61_m

3-hydroxyacyl-[acyl-carrier-protein] dehydratase (C6:1(2E) forming)(mitochondrial)

3HAD81_m

3-hydroxyacyl-[acyl-carrier-protein] dehydratase (C8:1(2E) forming)(mitochondrial)

3HBCOAHLm

3-hydroxyisobutyryl-CoA hydrolase, mitochondrial

3NPHBH1_m

Hydroxylation of 3-nonaaprenyl-4-hydroxybenzoate (NADH)

3NPHBH2_m

Hydroxylation of 3-nonaaprenyl-4-hydroxybenzoate (NADP)

4HBZCOAFm

4 hydroxybenzoyl CoA formation

4HBZFm

4 hydroxybenzoate formation

ACCPF_m

Accp formation, mitochondria

ACN_a_m

Citrate hydro-lyase (cis-aconitate-forming)

ACN_b_m

Isocitrate hydro-lyase (cis-aconitate-forming)

AGMTm

Agmatinase (m)

AOX_m

Alternative oxidase, mitochondria

ASCBPOX_m

Ascorbate peroxidase

ATPPHm

ATP phosphohydrolase, mitochondria

ATPS4m

ATP synthase (four protons for one ATP)

BTNCCPP_m

Proteolysis of btnccp, mitochondria

BTNDm

Biotinidase (biotin), mitochondrial

CBL_m

Cystathionine beta-lyase

CCP2_m

Cytochrome c peroxidase, mitochondrial

CLM_m

Cardiolipin maturation

COQ6_m

Ubiquinone biosynthesis monooxgenase COQ6

COQ7_m

Ubiquinone biosynthesis COQ7

CPS_m

Carbamoyl phosphate synthase (ammonia)

CSm

Citrate synthase

CYOO6m

Cytochrome c oxidase Complex IV

DHAD1m

Dihydroxy acid dehydratase 2 3 dihydroxy 3 methylbutanoate mitochondrial

DMGDHm

Dimethylglycine dehydrogenase, mitochondrial

ECH102_2E6Z_m

Enoyl-CoA hydratase (10:2(2E,6Z))

ECH102_2E7Z_m

Enoyl-CoA hydratase (10:2(2E,7Z))

ECH103_2E6Z9Z_m

Enoyl-CoA hydratase (10:3(2E,6Z,9Z))

ECH122_2E5Z_m

Enoyl-CoA hydratase (12:2(2E,5Z))

ECH122_2E6Z_m

Enoyl-CoA hydratase (12:2(2E,6Z))

ECH123_2E5Z8Z_m

Enoyl-CoA hydratase (12:3(2E,5Z,8Z))

ECH123_2E6Z9Z_m

Enoyl-CoA hydratase (12:3(2E,6Z,9Z))

ECH124_2E5Z8Z11Z_m

Enoyl-CoA hydratase (12:4(2E,5Z,8Z,11Z))

ECH142_2E5Z_m

Enoyl-CoA hydratase (14:2(2E,5Z))

ECH142_2E7Z_m

Enoyl-CoA hydratase (14:2(2E,7Z))

ECH143_2E5Z8Z_m

Enoyl-CoA hydratase (14:3(2E,5Z,8Z))

ECH143_2E7Z10Z_m

Enoyl-CoA hydratase (14:3(2E,7Z,10Z))

ECH144_2E5Z8Z11Z_m

Enoyl-CoA hydratase (14:4(2E,5Z,8Z,11Z))

ECH144_2E7Z10Z13Z_m

Enoyl-CoA hydratase (14:4(2E,7Z,10Z,13Z))

ECH162_2E7Z_m

Enoyl-CoA hydratase (16:2(2E,7Z))

ECH162_2E9Z_m

Enoyl-CoA hydratase (16:2(2E,9Z))

ECH163_2E7Z10Z_m

Enoyl-CoA hydratase (16:3(2E,7Z,10Z))

ECH163_2E9Z12Z_m

Enoyl-CoA hydratase (16:3(2E,9Z,12Z))

ECH164_2E6Z9Z12Z_m

Enoyl-CoA hydratase (16:4(2E,6Z,9Z,12Z))

ECH164_2E7Z10Z13Z_m

Enoyl-CoA hydratase (16:4(2E,7Z,10Z,13Z))

ECH165_2E6Z9Z12Z15Z_m

Enoyl-CoA hydratase (16:5(2E,6Z,9Z,12Z,15Z))

ECH181_2E_m

Enoyl-CoA hydratase (18:1)(2E)

ECH182_2E9Z_m

Enoyl-CoA hydratase (18:2(2E,9Z))

ECH183_2E9Z12Z_m

Enoyl-CoA hydratase (18:3(2E,9Z,12Z))

ECH184_2E6Z9Z12Z_m

Enoyl-CoA hydratase (18:4(2E,6Z,9Z,12Z))

ECH184_2E9Z12Z15Z_m

Enoyl-CoA hydratase (18:4(2E,9Z,12Z,15Z))

ECH62_2E5Z_m

Enoyl-CoA hydratase (6:2(2E,5Z))

ECH82_2E5Z_m

Enoyl-CoA hydratase (8:2(2E,5Z))

ECH82_2E7Z_m

Enoyl-CoA hydratase (8:2(2E,7Z))

ECOAH12m

Enoyl-coa hydratase, 3-Hydroxyisobutyryl-CoA forming

ECOAH1m

3-Hydroxybutanoyl-CoA hydro-lyase, mitochondria

ECOAH2m

Enoyl-CoA hydratase (C6:0)

ECOAH3m

Enoyl-CoA hydratase (C8:0)

ECOAH4m

Enoyl-CoA hydratase (C10:0)

ECOAH5m

Enoyl-CoA hydratase (C12:0)

ECOAH6m

Enoyl-CoA hydratase (C14:0)

ECOAH7m

Enoyl-CoA hydratase (C16:0)

ECOAH9m

Enoyl-coa hydratase, 3-Hydroxy-2-methylbutyryl-CoA forming

EDD_m

6-phospho-d-gluconate hydro-lyase

ENOm

Enolase, mitochondria

FA160ACPH_m

Fatty-acyl-ACP hydrolase (n-C16:0)

FAOXC70_m

Beta oxidation (odd chain) C(7:0)

FUMm

Fumarase mitochondrial

G5SADrm

L glutamate 5 semialdehyde dehydratase reversible mitochondrial

GDHm

Glutamate dehydrogenase, mitochondria

GHMT2rm

Glycine hydroxymethyltransferase reversible mitochondrial

GLUDym

Glutamate dehydrogenase (NADP), mitochondrial

H2Otm

H2O transport mitochondrial

HCO3Em

HCO3 equilibration reaction

HEMEASM_m

Heme a synthase (mitochondria)

HMGCOASm

Hydroxymethylglutaryl CoA synthase mitochondrial

HTHBDH_m

4a-hydroxytetrahydrobiopterin dehydratase

MGCHrm

Methylglutaconyl-coa hydratase

MI3PP_m

1D-myo-Inositol 3-phosphate phosphohydrolase

MTAN_m

Methylthioadenosine nucleosidase - adenosylhomocysteine nucleosidase

MTMOHT

5,10-Methylenetetrahydrofolate:3-methyl-2-oxobutanoate hydroxymethyltransferase

OXOGAH_m

2-Oxoglutaramate amidohydrolase

OXOSUCAH_m

2-Oxosuccinamate amidohydrolase

P5CDm

1 pyrroline 5 carboxylate dehydrogenase mitochondrial

PEPC_m

Phosphoenolpyruvate carboxylase

PGPP_PALM_PALM_m

Phosphatidylglycerol phosphate phosphatase (16:0/16:0) mitochondria

PIMACPS_m

Pimeloyl-[acyl-carrier protein] synthase

PPAm

Inorganic diphosphatase

PSP_m

Phosphoserine phosphatase

QULNS_m

Quinolinate synthase

r0142

Sulfite:oxygen oxidoreductase Sulfur metabolism EC:1.8.3.1

r0179

Succinate-semialdehyde:NADP+ oxidoreductase Glutamate metabolism / Tyrosine metabolism / Butanoate metabolism EC:1.2.1.16

SSALxm

Succinate-semialdehyde:NAD+ oxidoreductase, mitochondria

T4HCINNMFM

4 hydroxycinnamate formation

THFATm

Tetrahydrofolate aminomethyltransferase mitochondrial

TMABDH1_m

Trimethylammoniobutanal dehydrogenase

UREASE_m

Urease, mitochondria