3HBCOAHLm

3-hydroxyisobutyryl-CoA hydrolase, mitochondrial

3MOBt2im

3-methyl-2-oxobutanoate mitochondrial transport via proton symport

3MOPt2im

3-Methyl-2-oxopentanoate mitochondrial transport via proton symport

4MOPt2im

4-methyl-2-oxopentanoate mitochondrial transport via proton symport

AASAD3m

L-aminoadipate-semialdehyde dehydrogenase (NADH), mitochondrial

ALASm

5 aminolevulinate synthase

ATPS4m

ATP synthase (four protons for one ATP)

CBPSam

Carbamoyl-phosphate synthase (ammonia) (mitochondria

CSm

Citrate synthase

CYANSTm

Cyanide sulfurtransferase, mitochondrial

CYOOm2

Cytochromecoxidase,mitochondrialComplexIV

CYOR_u10m

Ubiquinol-6 cytochrome c reductase, Complex III

FAOXC160

Beta oxidation of long chain fatty acid

FAOXC16080m

Beta oxidation of long chain fatty acid

FAOXC180

Beta oxidation of long chain fatty acid

FAOXC1811603m

Beta oxidation fatty acid

FAOXC182806m

Beta oxidation of fatty acid

FAOXC204

Beta oxidation of long chain fatty acid

FAOXC80

Beta oxidation of med/long chain fatty acid

FCLTm

Ferrochelatase mitochondrial

FE2tm

Iron (II) transport

FPGS7m

Folylpolyglutamate synthetase (10fthf), mitochondrial

FPGS8m

Folylpolyglutamate synthetase (10fthf), mitochondrial

FPGS9m

Folylpolyglutamate synthetase (10fthf), mitochondrial

G5SADrm

L glutamate 5 semialdehyde dehydratase reversible mitochondrial

GDHm

Glutamate dehydrogenase, mitochondria

GLUTCOADHm

Glutaryl-CoA dehydrogenase (mitochondria)

GTHOm

Glutathione oxidoreductase

HACD1m

3-Hydroxybutanoyl-CoA:NAD+ oxidoreductase, mitochondria

HACD9m

(2S,3S)-3-hydroxy-2-methylbutanoyl-CoA:NAD+ oxidoreductase

HCO3Em

HCO3 equilibration reaction

HIBDm

3-hydroxyisobutyrate dehydrogenase, mitochondrial

LYStm

Lysine mitochondrial transport via ornithine carrier

MCCCrm

Methylcrotonoyl-CoA carboxylase, mitochondrial

MDHm

Malate dehydrogenase mitochondrial

MMTSADm

Malonate-semialdehyde dehydrogenase (acetylating), mitochondrial

MTHFCm

Methenyltetrahydrifikate cyclohydrolase mitochondrial

NADH2_u10m

NADH dehydrogenase, mitochondrial

OCBTm

Ornithine carbamoyltransferase, irreversible

ORNt3m

Ornithine mitochondrial transport via proton antiport

ORNt4m

Ornithine mitochondrial transport exchange with citruline

P5CRm

Pyrroline-5-carboxylate reductase, mitochondria

P5CRxm

Pyrroline-5-carboxylate reductase (m)

PIt2m_2

Phosphate mitochondrial transport via proton symport

PPCOACm

Propionyl-CoA carboxylase, mitochondrial

PROD2m

Proline dehydrogenase (m)

PYRt2m

Pyruvate mitochondrial transport via proton symport

SACCD3m

Saccharopine dehydrogenase (NADP, L-lysine forming), mitochondrial

SACCD4m

Saccharopine dehydrogenase (NAD, L-glutamate forming), mitochondrial

SPODMm

Superoxide dismutase

SSALxm

Succinate-semialdehyde:NAD+ oxidoreductase, mitochondria